Marfan's syndrome presenting as bilateral spontaneous pneumothorax.
نویسنده
چکیده
A case of bilateral spontaneous pneumothorax in a 14-year-old girl with previously undiagnosed Marfan's syndrome is described. The pulmonary abnormalities of Marfan's syndrome are not commonly encountered and bilateral pneumothorax is itself a rare event which, in most instances, has been reported following invasive procedures.
منابع مشابه
Bronchiectasis and Marfan's syndrome.
Marfan's syndrome is a rare hereditary disorder characterized by skeletal, cardiovascular and ocular abnormalities. Pulmonary abnormalities occur in approximately 10% of patients the commonest being spontaneous pneumothorax and emphysema. A patient is described who had Marfan's syndrome and bronchiectasis, an association only described on 2 previous occasions in the literature.
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ورودعنوان ژورنال:
- Postgraduate medical journal
دوره 57 666 شماره
صفحات -
تاریخ انتشار 1981